Alkaptonuria (AKU) AKU is a rare metabolic disorder characterized by the accumulation of homogentisic acid, which leads to a condition known as “black urine disease” due to urine turning dark ...
Low phenylalanine (PHE), glycomacropeptide-based protein substitute (GMP) is an alternative to traditional L-amino acid supplements (AA) used in the dietary management of phenylketonuria (PKU). In ...